C3 glomerulopathy disease

Can Huzmeli; Mehmet Hadi Akkus; Ferhan Candan

doi:10.7197/223.vi.407563

TR EN

C3 glomerulopati hastalığı

Öz

C3 glomerulopati (C3G), kompleman aktivasyonunun anormal kontrolü ile oluşan bir grup böbrek hastalığını kapsayan yakın zamanda tanımlanmış bir hastalıktır. C3G glomerullerde immunoglobulin birikiminin trace ve yokluğu ile dominant olarak kompleman C3 birikimi ile karakterizedir. C3G C3 glomerulonefrit (C3GN) ve Dens Deposit Hastalığı (DDD) diye iki grup hastalıktan oluşmaktadır. DDD ve C3GN nadir görülmektedir ve her iki hastalık hem çocuklarda hemde erişkinlerde görülmektedir. C3G spesifik tedavisinde, plazmaferez, immünsüpresif tedavi ve kompleman inhibitörlerini içermektedir.

Anahtar Kelimeler

C3 glomerulopati,C3 glomerulonefrit,dens deposit hastaliği,kompleman bozuklukları

References

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Details

Primary Language

English

Subjects

Health Care Administration

Journal Section

Review

Authors

Can Huzmeli ^*

Mehmet Hadi Akkus

Ferhan Candan

Publication Date

March 20, 2018

Submission Date

January 6, 2018

Acceptance Date

January 23, 2018

Published in Issue

Year 1970 Volume: 40 Number: 1

DOI

https://doi.org/10.7197/223.vi.407563

IZ

https://izlik.org/JA94SA47HE

Cite

RIS / Bibtex

AMA

1.Huzmeli C, Akkus MH, Candan F. C3 glomerulopathy disease. CMJ. 2018;40(1):1-8. doi:10.7197/223.vi.407563

C3 glomerulopathy disease

C3 glomerulopati hastalığı

Öz

Anahtar Kelimeler