Öz
Henoch-Schönlein purpura, leukocytoclastic vasculitis is the most common vasculitis of childhood. Immunoglobulin-A accumulates in the small veins of the skin, joints, gastrointestinal tract and kidney. The involvement of the skin in palpable purpuric rash is usually the first finding and basically shows the lower extremities and hips. Joints can be affected, kidneys can be affected. Complaints of gastrointestinal system usually occur one week after purpuric rash. The most common clinical features of the digestive system are abdominal pain and vomiting. The incidence of Intussusception in digestive tract involvement is about 1-5%. However, intussusception is not the first symptom. In our case, abdominal pain and Intussusception are the first findings. Typical rash appeared three days after operative. Second case in literature.
Anahtar Kelimeler
Henoch-Schonlein purpura Intussusception children vasculitis
Destekleyen Kurum
no
Proje Numarası
no
Kaynakça
- Stacy P. Ardoin EF. Vasculitis syndromes. In: Nelson Textbook of Pediatrics (Eds RM Kliegman, JWS Geme, NF Schor, RE Behrman):867-76. Philadelphia, Elsevier Saunders, 2011.
- S.Barron K. Vasculitis. In: Rudolph's Pediatrics (Eds CD. Rudolph, AM Rudolph, GE Lister, LR. First, AA. Gershon):810-2. New York, McGraw-Hill, 2011.
- Schaefer B, Soprano C. Five-year-old boy presenting with severe back pain, swelling, and refusal to walk. Clin Pediatr. 2014;53:95-7.
- Yang YH, Yu HH, Chiang BL. The diagnosis and classification of Henoch–Schönlein purpura: an updated review. Autoimmun Rev. 2014;13:355-8.
- Altınkaynak S, Ertekin V, Selimoglu MA. Association of Henoch-Schonlein purpura and hepatitis A. Journal of Emergency Medicine. 2006;30:219-20.
- Aydın M, Demirol M, Kurt A, Kurt N, Yılmaz E. The evaluation of our patients with Henoch-Schönlein purpura. Çocuk Dergisi. 2005;5:249-53.
- Trapani S, Micheli A, Grisolia F, Resti M, Chiappini E, Falcini F et al., Henoch Schonlein purpura in childhood: epidemiological and clinical analysis of 150 cases over a 5-year period and review of literature. Semin Arthritis Rheum. 2005;35:143-53.
- Özdemir H, Işik S, Buyan N, Hasanoglu E. Sonographic demonstration of intestinal involvement in Henoch-Schönlein syndrome. Eur J Radiol. 1995;20:32-4.
- Kim KY. Henoch-Schönlein purpura presenting as intussusception. Korean J Gastroenterol. 2017;69:372-6.
Öz
Henoch-Schönlein purpurası, çocukluk çağının en sık görülen lökositoklastik vaskülitidir. Derinin küçük damarlarında, eklemlerde, gastrointestinal sistemde ve böbreklerde immünoglobulin A birikir. Ciltte palpe edilebilen purpura genellikle ilk bulgudur ve genellikle alt ekstremiteler ve kalçada görülür. Eklemler etkilenebilir, böbrekler etkilenebilir. Gastrointestinal sistem şikayetleri genellikle purpurik döküntüden bir hafta sonra ortaya çıkar. Sindirim sisteminin en sık görülen klinik özellikleri karın ağrısı ve kusmadır. Sindirim sisteminin tutulumunda intussusepsiyon insidansı yaklaşık % 1-5' tir. Ancak, intussusepsiyon ilk belirti değildir. Bizim olgumuzda karın ağrısı ve intussusepsiyon ilk bulgulardır. Operasyondan üç gün sonra tipik döküntüler gözlenmiştir.
Anahtar Kelimeler
Henoch-Schonlein purpurası intussusepsiyon çocuklar vaskülit
Proje Numarası
no
Kaynakça
- Stacy P. Ardoin EF. Vasculitis syndromes. In: Nelson Textbook of Pediatrics (Eds RM Kliegman, JWS Geme, NF Schor, RE Behrman):867-76. Philadelphia, Elsevier Saunders, 2011.
- S.Barron K. Vasculitis. In: Rudolph's Pediatrics (Eds CD. Rudolph, AM Rudolph, GE Lister, LR. First, AA. Gershon):810-2. New York, McGraw-Hill, 2011.
- Schaefer B, Soprano C. Five-year-old boy presenting with severe back pain, swelling, and refusal to walk. Clin Pediatr. 2014;53:95-7.
- Yang YH, Yu HH, Chiang BL. The diagnosis and classification of Henoch–Schönlein purpura: an updated review. Autoimmun Rev. 2014;13:355-8.
- Altınkaynak S, Ertekin V, Selimoglu MA. Association of Henoch-Schonlein purpura and hepatitis A. Journal of Emergency Medicine. 2006;30:219-20.
- Aydın M, Demirol M, Kurt A, Kurt N, Yılmaz E. The evaluation of our patients with Henoch-Schönlein purpura. Çocuk Dergisi. 2005;5:249-53.
- Trapani S, Micheli A, Grisolia F, Resti M, Chiappini E, Falcini F et al., Henoch Schonlein purpura in childhood: epidemiological and clinical analysis of 150 cases over a 5-year period and review of literature. Semin Arthritis Rheum. 2005;35:143-53.
- Özdemir H, Işik S, Buyan N, Hasanoglu E. Sonographic demonstration of intestinal involvement in Henoch-Schönlein syndrome. Eur J Radiol. 1995;20:32-4.
- Kim KY. Henoch-Schönlein purpura presenting as intussusception. Korean J Gastroenterol. 2017;69:372-6.
Ayrıntılar
| Birincil Dil | İngilizce |
|---|---|
| Konular | Klinik Tıp Bilimleri |
| Bölüm | Editöre Mektup |
| Yazarlar | |
| Proje Numarası | no |
| Yayımlanma Tarihi | 31 Mart 2022 |
| Kabul Tarihi | 4 Şubat 2022 |
| Yayımlandığı Sayı | Yıl 2022 Cilt: 47 Sayı: 1 |
