Öz
İntakt ventriküler septumun eşlik ettiği pulmoner atrezi nadir görülen kardiyak bir malformasyondur. 10.000 canlı doğumda 0,58 oranında görülür. Ağır sağ kalp hipoplazisi olan vakalarının çoğunda prognoz kötü olduğundan erken tanı konması önemlidir.
Pulmonary atresia with intact ventricular septum is a rare cardiac malformation which is present at live birth of 0.58 per 10,000. Because of the prognosis is poor in most severe right heart hypoplasia cases,early diagnosis is critical.Konjenital kalp anomalileri perinatal mortalitenin önde gelen nedenlerinden biridir. Canlı doğumların %0,6' sı ve ölü doğumların % 10' unda konjenital kalp anomalilerine rastlanmaktadır (Fröber ve ark., 2001).
Anahtar Kelimeler
Pulmoner Atrezi İntakt Ventriküler Septum Hipoplastik Sağ Kalp
Kaynakça
- Arzt, W., Tulzer, G., Aigner, M., Mair, R., Hafner, E., 2003. Invasive intrauterine treatment of pulmonary atresia/intact ventricular septum with heart failure. Ultrasound Obstet. Gynecol. 21, 186-188.
- Berning, R.A., Silverman, N.H., Villegas, M., Sahn, D.J., Martin, G.R., Rice, M.J., 1996. Reversed shunting across the ductus arterio-sus or atrial septum in utero heralds severe congenital heart disease. Coll. Cardiol. 27, 481-486.
- Daubeney, P.E., Sharland, G.K, Cook, A.C., Keeton, B.R., Anderson, R.H., Webber, S.A., 1998. UK and Eire collaborative study of pulmonary atresia with intact ventricular septum. Pulmonary atresia with intact ventricular septum. Impact of fetal echocardiog- raphy on incidence at birth and postnatal outcome. Circulation. 98, 562-566.
- Freedom, R.N., Dische, M.R, Rowe, R.D., 1978. The tricuspid valve in pulmonary atresia and intact ventricular septum: A morpho- logical study of 60 cases. Arch. Pathol. Lab. Med. 102, 28-31.
- Fröber, R., Kohoutek, T., Kähler, C., Beensen, V., Hauschild, R., Schulze, E., Linss, W., 2001. Pulmonary atresia with hypoplastic right ventricle. A Clinical Embriyological Study. Fetal Diagnosis and Therapy. 16, 274-279.
- Fröber, R., Kohoutek, T., Kähler, C.H., 2006. Echocardiographic Predictors of Outcome in Fetuses with Pulmonary Atresia with Intact Ventricular Septum. J. Am. Society Echocardiog. 19, 1393-1400.
- Hornberger, L.K., Benacerraf, B.R., Bromley, B.S., Spevak, P.J., Sanders, S.P., 1994. Prenatal detection of severe right ventricular outflow tract obstruction pulmonary stenosis and pulmonary atresia. Ultrasound Med. 13, 743-750.
- Makato, N., Yoshıo, M., Masoto, K., 1999. Echocardiographic findings of pulmonary atresia or critical pulmonary stenosis and intact ventricular septum in utero. Pediatr. Int. 41, 716-721.
- Maeno, Y.V., Boutin, C., Hornberger, L.K, McCrindle, B.W., Cavallé-Garrido, T., Gladman, G., Smallhorn, J.F., 1999. Prenatal diagnosis of right ventricular outflow tract obstruction with intact ventricular septum, and detection of ventriculocoronary con- nections. Heart. 81, 661-668.
- Todros, T., Paladini, D., Chiappa, E., Russo, M.G., Gaglioti, P., Pacileo, G., Cau, M.A., Martinelli, P., 2003. Pulmonary stenosis and atresia with intact ventricular septum during prenatal life.Ultrasound Obstet. Gynecol. 21, 228-233.
Öz
Kaynakça
- Arzt, W., Tulzer, G., Aigner, M., Mair, R., Hafner, E., 2003. Invasive intrauterine treatment of pulmonary atresia/intact ventricular septum with heart failure. Ultrasound Obstet. Gynecol. 21, 186-188.
- Berning, R.A., Silverman, N.H., Villegas, M., Sahn, D.J., Martin, G.R., Rice, M.J., 1996. Reversed shunting across the ductus arterio-sus or atrial septum in utero heralds severe congenital heart disease. Coll. Cardiol. 27, 481-486.
- Daubeney, P.E., Sharland, G.K, Cook, A.C., Keeton, B.R., Anderson, R.H., Webber, S.A., 1998. UK and Eire collaborative study of pulmonary atresia with intact ventricular septum. Pulmonary atresia with intact ventricular septum. Impact of fetal echocardiog- raphy on incidence at birth and postnatal outcome. Circulation. 98, 562-566.
- Freedom, R.N., Dische, M.R, Rowe, R.D., 1978. The tricuspid valve in pulmonary atresia and intact ventricular septum: A morpho- logical study of 60 cases. Arch. Pathol. Lab. Med. 102, 28-31.
- Fröber, R., Kohoutek, T., Kähler, C., Beensen, V., Hauschild, R., Schulze, E., Linss, W., 2001. Pulmonary atresia with hypoplastic right ventricle. A Clinical Embriyological Study. Fetal Diagnosis and Therapy. 16, 274-279.
- Fröber, R., Kohoutek, T., Kähler, C.H., 2006. Echocardiographic Predictors of Outcome in Fetuses with Pulmonary Atresia with Intact Ventricular Septum. J. Am. Society Echocardiog. 19, 1393-1400.
- Hornberger, L.K., Benacerraf, B.R., Bromley, B.S., Spevak, P.J., Sanders, S.P., 1994. Prenatal detection of severe right ventricular outflow tract obstruction pulmonary stenosis and pulmonary atresia. Ultrasound Med. 13, 743-750.
- Makato, N., Yoshıo, M., Masoto, K., 1999. Echocardiographic findings of pulmonary atresia or critical pulmonary stenosis and intact ventricular septum in utero. Pediatr. Int. 41, 716-721.
- Maeno, Y.V., Boutin, C., Hornberger, L.K, McCrindle, B.W., Cavallé-Garrido, T., Gladman, G., Smallhorn, J.F., 1999. Prenatal diagnosis of right ventricular outflow tract obstruction with intact ventricular septum, and detection of ventriculocoronary con- nections. Heart. 81, 661-668.
- Todros, T., Paladini, D., Chiappa, E., Russo, M.G., Gaglioti, P., Pacileo, G., Cau, M.A., Martinelli, P., 2003. Pulmonary stenosis and atresia with intact ventricular septum during prenatal life.Ultrasound Obstet. Gynecol. 21, 228-233.
Ayrıntılar
| Birincil Dil | İngilizce |
|---|---|
| Konular | Sağlık Kurumları Yönetimi |
| Bölüm | Surgery Medical Sciences |
| Yazarlar | |
| Yayımlanma Tarihi | 30 Aralık 2010 |
| Gönderilme Tarihi | 10 Ocak 2011 |
| Yayımlandığı Sayı | Yıl 2009 Cilt: 26 Sayı: 4 |
Kaynak Göster
This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.