Foix-Chavany-Marie syndrome due to a unilateral opercular infarction
Abstract
Bilateral paralysis of facial, pharyngeal, lingual, and masticatory muscles with automatic-voluntary dissociation characterizes Foix-Chavany-Marie syndrome (FCMS). The syndrome is a rare neurological disorder which usually develops secondary to cerebrovascular accidents affecting bilateral opercular regions, typically as a result of subsequent strokes. A 75-year-old woman presented with acute onset of inability to speak and swallow. Neurological examination demonstrated bilateral palsy of lower motor cranial nerves with preservation of reflex and automatic movements. Magnetic resonance images of the brain showed an acute right frontal opercular infarction and old subcortical lacunar infarctions in the bilateral hemispheres. Although FCMS occurs due to bilateral opercular lesions, rarely unilateral opercular lesion accompanied by contralateral subcortical lesions may cause the typical clinical features of the syndrome.
Keywords
References
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Details
Primary Language
English
Subjects
Health Care Administration
Journal Section
Research Article
Publication Date
June 11, 2010
Submission Date
December 8, 2009
Acceptance Date
-
Published in Issue
Year 2010 Volume: 32 Number: 2