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AKCİĞERİN NADİR BENİGN TÜMÖRÜ: Perivasküler epiteloid tümör (PEComa)

Year 2025, Volume: 47 Issue: 3, 29 - 33, 30.09.2025

Abstract

Thanks

3. Uluslararası Kanser Günleri'nin başkanı olan Prof.Dr.Zekiye HASBEK ve dizenleme kuruluna teşekkür ederim.

References

  • 1. Policarpio-Nicolas ML, Covell J, Bregman S, Atkins K. Fine needle aspiration cytology of clear cell "sugar" tumor (PEComa) of the lung: report of a case. Diagn Cytopathol. 2008;36(2):89-93. doi:10.1002/dc.20647
  • 2. Doğan H. Küçük Hücreli Akciğer Kanserlerinde Güncel Tani Ve Tedavi Yaklaşimlar: Küçük Hücreli Akciğer Kanserinde Yaygın Evrede Palyatif Cerrahi Yaklaşımlar. 1.Baskı. Sivas Cumhuriyet Üniversitesi Rektörlük Matbaa;2024
  • 3. Vijayabhaskar R, Mehta SS, Deodhar KK, Pramesh CS, Mistry RC. PEComa of the lung. J Cancer Res Ther. 2010;6(1):109-111. doi:10.4103/0973-1482.63548
  • 4. Sen S, Senturk E, Kuman NK, Pabuscu E, Kacar F. PEComa (clear cell "sugar" tumor) of the lung: a benign tumor that presented with thrombocytosis. Ann Thorac Surg. 2009;88(6):2013-2015. doi:10.1016/j.athoracsur.2009.05.041
  • 5. Günlüoğlu ZM. Benign Akciğer Tümörleri, Torasik Cerrahi, 1. Baskı. İstanbul Tıp Kitapevleri, İstanbul; 2019
  • 6. Chen YB, Guo LC, Huang JA, Ji C, Ling CH. Clear cell tumor of the lung: a retrospective analysis. Am J Med Sci. 2014;347(1):50-53. doi:10.1097/MAJ.0b013e318295c821
  • 7. Selvaggi F, Risio D, Claudi R, et al. Malignant PEComa: a case report with emphasis on clinical and morphological criteria. BMC Surg. 2011;11:3. Published 2011 Jan 27. doi:10.1186/1471-2482-11-3
  • 8. O'Brien LM, Thuillier R, Tolan M, Fabre A. Clear cell 'sugar' tumour of the lung. BMJ Case Rep. 2021;14(2):e241698. Published 2021 Feb 26. doi:10.1136/bcr-2021-241698

Rare Benign Tumor of the Lung: Perivascular Epithelioid Tumor (Pecoma)

Year 2025, Volume: 47 Issue: 3, 29 - 33, 30.09.2025

Abstract

Perivascular epithelioid tumors (PEComas) are a group of mesenchymal tumors that include angiomyolipoma, lymphangiomyomatoasis, and clear cell tumors of the lung. So far, only 50 cases have been reported. The 'frozen section' was studied intraoperatively. However, since benign-malignant distinction could not be made, thoracotomy with middle lobectomy and mediastinal lymph node dissection was performed. In our case, it is aimed to contribute to the literature with the diagnosis and treatment of a rare clear cell tumor of the lung by performing a middle lobectomy on a 66-year-old female patient.
In conclusion, since the future behavior of these tumors is not clearly known, we recommend anatomical resection for these patients in cases where there is uncertainty in the 'frozen section' (1).

References

  • 1. Policarpio-Nicolas ML, Covell J, Bregman S, Atkins K. Fine needle aspiration cytology of clear cell "sugar" tumor (PEComa) of the lung: report of a case. Diagn Cytopathol. 2008;36(2):89-93. doi:10.1002/dc.20647
  • 2. Doğan H. Küçük Hücreli Akciğer Kanserlerinde Güncel Tani Ve Tedavi Yaklaşimlar: Küçük Hücreli Akciğer Kanserinde Yaygın Evrede Palyatif Cerrahi Yaklaşımlar. 1.Baskı. Sivas Cumhuriyet Üniversitesi Rektörlük Matbaa;2024
  • 3. Vijayabhaskar R, Mehta SS, Deodhar KK, Pramesh CS, Mistry RC. PEComa of the lung. J Cancer Res Ther. 2010;6(1):109-111. doi:10.4103/0973-1482.63548
  • 4. Sen S, Senturk E, Kuman NK, Pabuscu E, Kacar F. PEComa (clear cell "sugar" tumor) of the lung: a benign tumor that presented with thrombocytosis. Ann Thorac Surg. 2009;88(6):2013-2015. doi:10.1016/j.athoracsur.2009.05.041
  • 5. Günlüoğlu ZM. Benign Akciğer Tümörleri, Torasik Cerrahi, 1. Baskı. İstanbul Tıp Kitapevleri, İstanbul; 2019
  • 6. Chen YB, Guo LC, Huang JA, Ji C, Ling CH. Clear cell tumor of the lung: a retrospective analysis. Am J Med Sci. 2014;347(1):50-53. doi:10.1097/MAJ.0b013e318295c821
  • 7. Selvaggi F, Risio D, Claudi R, et al. Malignant PEComa: a case report with emphasis on clinical and morphological criteria. BMC Surg. 2011;11:3. Published 2011 Jan 27. doi:10.1186/1471-2482-11-3
  • 8. O'Brien LM, Thuillier R, Tolan M, Fabre A. Clear cell 'sugar' tumour of the lung. BMJ Case Rep. 2021;14(2):e241698. Published 2021 Feb 26. doi:10.1136/bcr-2021-241698
There are 8 citations in total.

Details

Primary Language English
Subjects Health Care Administration
Journal Section Case Reports
Authors

Mahmut Özbey 0000-0001-8641-1772

Gülgün Feyza Özatakan 0009-0007-1823-3506

Tülay Koç 0000-0001-8612-0238

Publication Date September 30, 2025
Acceptance Date July 18, 2025
Published in Issue Year 2025 Volume: 47 Issue: 3

Cite

AMA Özbey M, Özatakan GF, Koç T. Rare Benign Tumor of the Lung: Perivascular Epithelioid Tumor (Pecoma). CMJ. September 2025;47(3):29-33.