Management of Budd Chiari Syndrome by liver transplantation: A case report
Abstract
Abstract
Budd-Chiari syndrome (obstruction of venous drainage of the liver) may be idiopathic, due to thrombosis of the hepatic veins in thrombogenic states or be due to extrinsic compression. It is rare, but life-threatening, if left untreated. For patients with end-stage liver disease, liver transplantation should be considered. Orthotopic liver transplantation (OLT) is associated with the potential for massive blood loss, necessitating rapid infusion of large quantities of blood products. In these patients, hemodynamic instability can be dramatically diminished by inferior vena cava cross-clamping during OLT. There are few reports about living donor transplantations in Budd-Chiari case. We present a case of 27-year-old man, with a diagnosis of end-stage liver disease secondary to Budd-Chiari syndrome and underwent living OLT. Anaesthesia management, and follow-up of patients affected by this condition represent a challenge for anesthesiologists. The aim of this report is to discuss the potential options in the intraoperative management of patients with Budd-Chiari syndrome, who will undergo living OLT.
Keywords: Budd-Chiari syndrome, orthotopic liver transplantation, anaesthesia management
Keywords
References
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Details
Primary Language
English
Subjects
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Journal Section
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Publication Date
February 14, 2014
Submission Date
January 2, 2013
Acceptance Date
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Published in Issue
Year 2013 Volume: 35 Number: 4