Management of Budd Chiari Syndrome by liver transplantation: A case report
Abstract
Abstract
Budd-Chiari syndrome (obstruction of venous drainage of the liver) may be idiopathic, due to thrombosis of the hepatic veins in thrombogenic states or be due to extrinsic compression. It is rare, but life-threatening, if left untreated. For patients with end-stage liver disease, liver transplantation should be considered. Orthotopic liver transplantation (OLT) is associated with the potential for massive blood loss, necessitating rapid infusion of large quantities of blood products. In these patients, hemodynamic instability can be dramatically diminished by inferior vena cava cross-clamping during OLT. There are few reports about living donor transplantations in Budd-Chiari case. We present a case of 27-year-old man, with a diagnosis of end-stage liver disease secondary to Budd-Chiari syndrome and underwent living OLT. Anaesthesia management, and follow-up of patients affected by this condition represent a challenge for anesthesiologists. The aim of this report is to discuss the potential options in the intraoperative management of patients with Budd-Chiari syndrome, who will undergo living OLT.
Keywords: Budd-Chiari syndrome, orthotopic liver transplantation, anaesthesia management
Keywords
Kaynakça
- Choi GS, Park JB, Jung GO, Chun JM, Kim JM, Moon JI, Kwon CH, Kim SJ, Joh JW, Lee SK. Living donor liver transplantation in Budd-Chiari syndrome: A single-center experience. Transplant Proc 2010; 42: 839.
- Yoshimura N, Okajima H, Ushigome H, Sakamoto S, Fujiki M, Okamoto M. Current status of organ transplantation in Japan and worldwide. Surg Today 2010; 40: 514-25.
- Soyama A, Eguchi S, Yanaga K, Takatsuki M, Hidaka M, Kanematsu T. Living donor liver transplantation with extensive caval thrombectomy for acute-onchronic Budd-Chiari syndrome. Surg Today 2011; 41: 1026.
- Yamada T, Tanaka K, Ogura Y, Ko S, Nakajima Y, Takada Y, Uemoto S. Surgical techniques and long-term outcomes of living donor liver transplantation for Budd-Chiari syndrome. Am J Transplant 2006; 6: 2463-9.
- Menon KV, Shah V, Kamath PS. The Budd-Chiari syndrome. N Engl J Med 2004; 350: 578-85.
- Plessier A, Sibert A, Consigny Y, Hakime A, Zappa M, Denninger MH, Condat B, Farges O, Chagneau C, de Ledinghen V, Francoz C, Sauvanet A, Vilgrain V, Belghiti J, Durand F, Valla D. Aiming at minimal invasiveness as a therapeutic strategy for Budd-Chiari syndrome. Hepatology 2006; 44: 1308-16.
- Valla DC. Hepatic vein thrombosis (Budd-Chiari syndrome). Semin Liver Dis 2002; 22: 5-14.
- Cazals-Hatem D, Vilgrain V, Genin P, Denninger MH, Durand F, Belghiti J, Valla D, Degott C. Arterial and portal circulation and parenchymal changes in Budd-Chiari syndrome: A study in 17 explanted livers. Hepatology 2003; 37: 510
Ayrıntılar
Birincil Dil
İngilizce
Konular
-
Bölüm
-
Yayımlanma Tarihi
14 Şubat 2014
Gönderilme Tarihi
2 Ocak 2013
Kabul Tarihi
-
Yayımlandığı Sayı
Yıl 2013 Cilt: 35 Sayı: 4